Ebstien Anomaly with Cardiomegaly in a Paediatric Patient: Case Report

Ebstien anomaly is a rare heart problem present at birth and has a varied clinical course, it’s a congenital heart defect of the tricuspid valve. We hereby describe a 13-year-old child, was presented with history of Ebstien anomaly with Ostium secundum Atrial Septal Defect (OS ASD) was diagnosed at 1 year of age, but surgical correction was not done in early decade due to financial problem. At admission, child was in shock and saturation was not maintaining, Echocardiogram examination revealed Congenital Heart Disease (CHD), Ebstien anomaly, RA/ RV dilated, atrialised Right Ventricle (RV), Septal Tricuspid Leaflet (STL) displaced to the origin distance 5.6cm was noted, Grade 2+ Tricuspid Regurgitation (TR), Pulmonary Artery Systolic Pressure (PASP)-28 mmHg, no Pulmonary Arterial Hypertension (PAH), normal Biventricular function. Child needed immediate surgical correction. Child was discharged with referral letter to higher centre.